Vol. 1, Issue 1, Part A (2019)

Aicardi syndrome is a rare congenital disorder characterised by a triad of Callosal agenesis, infantile spasms and chorioretinal lacunae along with other congenital defects of the eyes, ribs, vertebrae and frequently associated with mental retardation and intractable seizures. The rare syndromes are challenge to mange by the physicians and when such patients are posted for any surgery same challenge is faced by the anesthesiologist. We report a case of Aicardi syndrome posted for oral rehabilitation procedure.